LysosomesGlucuronidaseMannosephosphatesAcetylglucosaminidaseReceptor, IGF Type 2Cathepsin DAcid PhosphataseHexosaminidasesMucolipidosesbeta-N-AcetylhexosaminidasesCerebroside-Sulfatasealpha-MannosidaseArylsulfatasesMannosidasesCathepsinsTransferases (Other Substituted Phosphate Groups)Lysosomal Storage Diseasesalpha-L-FucosidaseHydrolasesSulfatasesbeta-GlucosidaseHexosephosphatesalpha-GalactosidaseGalactosidasesVitamin A DeficiencyDeficiency DiseasesGlucosidasesZymosanIduronidaseGlucosylceramidaseCathepsin Balpha 1-Antitrypsin DeficiencyGaucher DiseaseVitamin B 12 DeficiencyGlycoside Hydrolasesalpha-GlucosidasesAmmonium ChlorideMucopolysaccharidosis ILiverFibroblastsCathepsin LVitamin D DeficiencyGlycogen Storage Disease Type IIEndocytosisFabry DiseaseFolic Acid DeficiencyPinocytosisCytochalasin Bbeta-GalactosidaseIgA DeficiencyThiamine DeficiencyGalactosylceramidaseOligosaccharidesGangliosidosesN-Acetylgalactosamine-4-SulfataseMice, KnockoutAspartylglucosylaminaseMethylmannosidesMannosyl-Glycoprotein Endo-beta-N-AcetylglucosaminidaseNeutrophilsPhagocytosisCathepsin CMucopolysaccharidosis IVCells, CulturedChondro-4-SulfataseMicroscopy, ElectronGolgi ApparatusMutationDictyosteliumMucopolysaccharidosesGlucosephosphate Dehydrogenase DeficiencyMacrophagesLeukodystrophy, Globoid CellEnzyme Replacement TherapyMannoseMagnesium DeficiencyMetabolism, Inborn ErrorsLeukodystrophy, MetachromaticCell CompartmentationAnemia, Iron-DeficiencyVitamin E DeficiencyDipeptidyl-Peptidases and Tripeptidyl-PeptidasesCell FractionationAscorbic Acid DeficiencyMice, Inbred C57BLMucopolysaccharidosis IIKineticsHexosaminidase AIduronate SulfataseThiolester HydrolasesCell LineMolecular Sequence DataImmunologic Deficiency SyndromesHistocytochemistryProtein C DeficiencyEnzyme PrecursorsIgG DeficiencyTay-Sachs DiseaseBiological TransportHydrogen-Ion Concentration