DeafnessHair Cells, AuditoryHairHair Cells, Auditory, InnerHair Cells, Auditory, OuterHair Cells, VestibularCochleaSaccule and UtricleOrgan of CortiHair FollicleEar, InnerHearing Loss, SensorineuralStereociliaHearingHearing LossEvoked Potentials, Auditory, Brain StemHair Cells, AmpullaHair ColorSpiral GanglionMechanotransduction, CellularBacterial Outer Membrane ProteinsHair DiseasesStria VascularisLateral Line SystemTranscription Factor Brn-3CHair RemovalCochlear DiseasesCochlear NerveVestibule, LabyrinthTectorial MembraneHair DyesEndolymphHair PreparationsAcoustic MaculaeNeomycinElectric CapacitanceHearing Loss, Noise-InducedAuditory ThresholdCochlear DuctRana catesbeianaCiliaCochlear Microphonic PotentialsGenes, RecessivePedigreeMutationBasilar MembraneTurtlesOtoacoustic Emissions, SpontaneousMicroscopy, Electron, ScanningConnexinsUsher SyndromesAcoustic StimulationAudiometryRod Cell Outer SegmentSyndromeGuinea PigsRegenerationZebrafishMechanoreceptorsHearing Loss, CentralNeurons, EfferentHearing Loss, UnilateralChinchillaAnimals, NewbornGentamicinsAlopeciaCochlear ImplantsHearing Loss, BilateralMolecular Sequence DataPyridinium CompoundsMembrane ProteinsKCNQ Potassium ChannelsVestibulocochlear NerveMembrane PotentialsCochlear ImplantationAnion Transport ProteinsAminoglycosidesHearing DisordersLabyrinth DiseasesEarConsanguinityAuditory PathwaysOtolithic MembraneChickensPhenotypeGerbillinaeSemicircular CanalsVestibular DiseasesMyosinsAudiometry, Pure-ToneAmino Acid SequenceMice, Mutant StrainsOrgan Culture TechniquesHearing TestsPatch-Clamp TechniquesMolecular Motor ProteinsEvoked Potentials, AuditoryElectrophysiologyMice, KnockoutCell Membrane