DeafnessHearing Loss, SensorineuralHearing LossCochleaPedigreeGenes, RecessiveEar, InnerEvoked Potentials, Auditory, Brain StemConnexinsSyndromeHearing Loss, UnilateralHair Cells, AuditoryStria VascularisSpiral GanglionHearingAudiometryCochlear ImplantsHearing Loss, BilateralConsanguinityCochlear ImplantationUsher SyndromesMutationLipreadingHearing TestsHearing Loss, CentralEndolymphSign LanguageWolfram SyndromeAuditory ThresholdWaardenburg SyndromeAudiometry, Pure-ToneCochlear NerveHypoparathyroidismOrgan of CortiHair Cells, Auditory, InnerVestibular DiseasesJervell-Lange Nielsen SyndromeStereociliaGenetic LinkageCochlear DiseasesTectorial MembraneDNA Mutational AnalysisHearing DisordersStapesPersons With Hearing ImpairmentsMutation, MissenseChromosome MappingTranscription Factor Brn-3CGenes, DominantHair ColorPhenotypeHearing AidsHearing Loss, ConductiveKCNQ Potassium ChannelsVestibular AqueductLabyrinth DiseasesIchthyosisAtaxiaGoiterTemporal BoneAbnormalities, MultipleCochlear DuctDNA, MitochondrialHair Cells, Auditory, OuterIntellectual DisabilityNephritis, HereditaryGenetic TestingQuestionnairesBulbar Palsy, ProgressiveAcoustic StimulationVestibule, LabyrinthEarBlindnessColobomaPrevalenceAuditory CortexHomozygoteMolecular Sequence DataAuditory PerceptionPoint MutationLod ScoreNational Institute on Deafness and Other Communication Disorders (U.S.)Keratoderma, PalmoplantarRisk FactorsFacial Paralysis