Carnitine O-PalmitoyltransferaseSerine C-PalmitoyltransferaseMalonyl Coenzyme APalmitoyl Coenzyme AAcyltransferasesSerineAcyl Coenzyme ACarnitineSphingolipidsCarnitine AcyltransferasesMitochondria, LiverHereditary Sensory and Autonomic NeuropathiesEpoxy CompoundsPalmitoylcarnitinePalmitatesStarvationFatty AcidsSerine EndopeptidasesPalmitic AcidKetone BodiesLiverCeramidesSubmitochondrial ParticlesMyoglobinuriaRats, Inbred StrainsLipoylationOxidation-ReductionMolecular Sequence DataSphingomonasAmino Acid SequenceKineticsSerine ProteasesSphingosine N-AcyltransferaseSphingosineSerine Proteinase InhibitorsCarnitine O-AcetyltransferaseMitochondria, MuscleLipid Metabolism, Inborn ErrorsIsoenzymesCoenzyme APalmitic AcidsDigitoninMicrobodiesCitrate (si)-SynthaseCycloserineIntracellular MembranesSphingomyelinsFatty Acids, MonounsaturatedMitochondria, HeartCaprylatesSubstrate SpecificityLipid MetabolismAcetylcarnitineAzetidinesGene Expression Regulation, EnzymologicEthers, CyclicAcetyl-CoA CarboxylaseRats, Inbred BUFBase SequencePhosphorylationOleic AcidsMitochondriaOleic AcidCeramidasesFumonisinsSequence Homology, Amino AcidAcyl-CoA OxidaseRNA, MessengerPichia3-Hydroxyacyl CoA DehydrogenasesMutationMuscle, SkeletalGlyoxylatesBinding SitesEsterificationBenzyl AlcoholAcyl-CoA Dehydrogenase, Long-ChainCoenzyme A LigasesDetergentsRats, WistarCatalysisMyocardiumBezafibrateCells, CulturedSphingomyelin PhosphodiesteraseBlotting, WesternTriglyceridesDiabetes Mellitus, ExperimentalCell LineClofibrateEnzyme InhibitorsRhabdomyolysisDiabetic KetoacidosisMutagenesis, Site-DirectedDNA, ComplementaryRats, Sprague-DawleyMicrosomesPPAR alphaAcyl-CoA DehydrogenaseCloning, Molecular