Cystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorFibrosisPostoperative ComplicationsPseudomonas InfectionsPseudomonas aeruginosaSweatSputumMice, Inbred CFTRBurkholderia InfectionsBurkholderia cepaciaChloridesEndomyocardial FibrosisTreatment OutcomeLungIdiopathic Pulmonary FibrosisRetrospective StudiesLiver CirrhosisExocrine Pancreatic InsufficiencyChloride ChannelsIntraoperative ComplicationsRespiratory MucosaLung DiseasesTobramycinNasal MucosaForced Expiratory VolumeNeonatal ScreeningPancreatinRetroperitoneal FibrosisTime FactorsRespiratory Function TestsBurkholderia cepacia complexPancreatic ExtractsBronchiectasisRespiratory SystemMutationAnti-Bacterial AgentsLung TransplantationEpithelial CellsFollow-Up StudiesProspective StudiesBronchiMucusDiabetes ComplicationsHeterozygote DetectionMeconiumExpectorantsBleomycinAlginatesDisease Models, AnimalInfant, NewbornRisk FactorsTracheaPancrelipaseAchromobacter denitrificansSeverity of Illness IndexPregnancy ComplicationsMucociliary ClearanceBurkholderia cenocepaciaChronic DiseaseSweat GlandsPhenotypeVital CapacityRespiratory Tract InfectionsAspergillosis, Allergic BronchopulmonaryAminophenolsLeukocyte ElastaseGenotypeIon TransportCell LineIntestinal ObstructionTomography, X-Ray ComputedOral Submucous FibrosisCells, CulturedBiopsyGenetic TestingLiver Cirrhosis, ExperimentalAdministration, InhalationEpitheliumBiological MarkersAmilorideDrainage, PosturalReoperationDisease ProgressionHexuronic AcidsMice, Inbred C57BLColistinRespiratory TherapyStenotrophomonas maltophiliaUreteral ObstructionMolecular Sequence DataHydroxyprolineGlucuronic AcidIncidenceIleusExocrine GlandsBronchopneumoniaPolymerase Chain ReactionBronchoalveolar Lavage FluidMucins