Electron Transport Complex IVElectron Transport Complex IMitochondriaCytochrome-c Oxidase DeficiencyElectron Transport Complex IIElectron Transport Complex IIICell RespirationElectron TransportOxidative PhosphorylationElectron Transport Chain Complex ProteinsMitochondrial ProteinsMitochondrial DiseasesLeigh DiseaseDNA, MitochondrialSodium AzideOxygen ConsumptionCitrate (si)-SynthaseMitochondria, HeartMitochondrial Proton-Translocating ATPasesMembrane Potential, MitochondrialSuccinate DehydrogenaseAntimycin ASuccinate Cytochrome c OxidoreductaseNADH DehydrogenaseCytochromes cReactive Oxygen SpeciesCardiolipinsMitochondria, MuscleGinsenosidesNAD(P)H Dehydrogenase (Quinone)Multienzyme ComplexesMitochondrial MembranesUbiquinoneConsanguinityUncoupling AgentsOxidoreductasesOxidation-ReductionOxidative StressCollagen Type IVAdenosine TriphosphateNADH, NADPH OxidoreductasesOxygenMutationElectrophoresis, Gel, Two-DimensionalMembrane ProteinsCells, CulturedHomozygoteProtein SubunitsChaperonin 60BrainMitochondria, LiverNitric OxideEnergy MetabolismBlotting, WesternRats, WistarMuscle, SkeletalMolecular Sequence DataRats, Sprague-DawleyAgingCell SurvivalCell LineAmino Acid SequenceMice, TransgenicApoptosisDNA Topoisomerase IVCarbonic Anhydrase IV