Electron Transport Complex ILeigh DiseaseMitochondrial DiseasesNADH DehydrogenaseNAD(P)H Dehydrogenase (Quinone)Mitochondrial EncephalomyopathiesMELAS SyndromeMitochondriaDNA, MitochondrialMetabolism, Inborn ErrorsOxidative PhosphorylationRotenoneMitochondrial MyopathiesNADH, NADPH OxidoreductasesFibroblastsHyperargininemiaMitochondria, MuscleMutationMitochondrial ProteinsComplement Factor IDNA Mutational AnalysisFatal OutcomePedigreeCarbamoyl-Phosphate Synthase I Deficiency DiseaseInfant, NewbornCell NucleusPhenotypeProtein C DeficiencyYarrowiaCells, CulturedConsanguinityHomozygoteProtein S DeficiencyMolecular Sequence DataMitochondria, HeartElectron TransportUbiquinoneElectron Transport Complex IIPoint MutationVitamin A DeficiencyQuinone ReductasesDeficiency DiseasesHeterozygoteElectron Transport Complex IIIBase SequenceSkinalpha 1-Antitrypsin DeficiencyAmino Acid SequenceVitamin B 12 DeficiencyProtein SubunitsVitamin D DeficiencyCell RespirationUncoupling AgentsFolic Acid DeficiencyElectron Transport Chain Complex ProteinsIgA DeficiencyProton PumpsThiamine DeficiencySubmitochondrial ParticlesSecosteroidsReactive Oxygen SpeciesOxidation-ReductionGlucosephosphate Dehydrogenase DeficiencyMice, KnockoutIron-Sulfur ProteinsSuccinic AcidMagnesium DeficiencyInterleukin-11 Receptor alpha SubunitVitamin E DeficiencyAscorbic Acid DeficiencyOxygen Consumption