CitrullineCarbamyl PhosphateCarbamoyl-Phosphate Synthase (Ammonia)Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing)OrnithineOrnithine CarbamoyltransferaseArginineCarbamatesDihydroorotaseAspartate CarbamoyltransferaseLigasesAmmoniaGlutaminePhosphotransferasesCitrullusOrotic AcidHydrolasesMitochondria, LiverUreaNitrogen IsotopesKineticsGlutamatesArgininosuccinate SynthaseGlutaminaseNitric Oxide SynthaseCitrullinemiaArgininosuccinate LyaseAmino AcidsAmino Acid Metabolism, Inborn ErrorsCarboxyl and Carbamoyl TransferasesArginaseProlineArgininosuccinic AcidGlyoxalNitric OxideUracil NucleotidesAmino Acid OxidoreductasesUracilUridine MonophosphatePhosphoribosyl PyrophosphateAcetyleneEscherichia coliCatecholamine Plasma Membrane Transport ProteinsMouth AbnormalitiesAdenosine TriphosphateLiverAmino-Acid N-AcetyltransferaseShort Bowel SyndromeOligomycinsOrganophosphorus CompoundsOrganophosphatesEnterocytesAmino Acids, DiaminoBicarbonatesRenal AminoaciduriasAspartic AcidOrnithine-Oxo-Acid TransaminasePhosphonoacetic AcidAmino Acid Transport Systems, BasicPhosphatesOrnithine Carbamoyltransferase Deficiency DiseaseCarbon IsotopesBiopterinNitritesPhenylbutyrates