The most popular theory holds that cor triatriatum sinister occurs when the common pulmonary vein fails to incorporate the pulmonary circulation into the left atrium and the common pulmonary venous ostium remains narrow (malincorporation theory). (medscape.com)
Uncommonly associated defects include atrial septal defect, cor triatriatum, left superior vena cava, unroofed coronary sinus, partial anomalous pulmonary venous drainage, pulmonary venous obstruction, double-orifice mitral valve, and Wolff-Parkinson-White syndrome. (medscape.com)
Transcatheter right ventricular outflow tract stent implantation in a child with pentalogy of Cantrell, double outlet right ventricle, and severe pulmonary stenosis. (ucdenver.edu)
Triatrial heart2
Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is subdivided by a thin membrane, resulting in three atrial chambers (hence the name). (wikipedia.org)
[ 1 ] cor triatriatum, that is, a heart with three atria (triatrial heart), is a congenital anomaly in which the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is divided into two compartments by a fold of tissue, a membrane, or a fibromuscular band. (medscape.com)
Aortic2
At autopsy one fetus demonstrated nuchal edema, mild hydronephrosis, and cor triatriatum dexter associated with ventricular septal defect and tubular hypoplasia of the aortic arch. (regionh.dk)
Chohan A, Abraham CJ, Ward K, Ponniah K, Salkini A , Burkhart HM , Mir A . Isolated ostial left main coronary artery stenosis causing ischemic cardiomyopathy in a child with bicuspid aortic valve: Role of echocardiography in diagnosis and follow-up. (ouhsc.edu)
Dextrum1
Cor triatriatum dextrum is extremely rare and results from the complete persistence of the right sinus valve of the embryonic heart. (wikipedia.org)
Sinistrum1
Cor triatriatum sinistrum is more common. (wikipedia.org)
Mitral2
therefore, awareness of the problem and careful echocardiographic screening are important in all children with mitral valve disease. (medscape.com)
Presentation, natural history, and outcome in children and adolescents with double orifice mitral valve. (medscape.com)
Dexter4
The other fetus demonstrated severe nuchal edema, and cor triatriatum dexter was the only malformation. (regionh.dk)
Cor triatriatum dexter is a rare cardiac malformation characterized by division of the right atrium into 2 compartments by a usually fenestrated membrane representing remnants of the right valve of the embryonic sinus venosus. (regionh.dk)
Maroun, LL , Graem, N & Skibsted, L 2008, ' Fetal cor triatriatum dexter: a report of two cases associated with nuchal edema in early second trimester ', Pediatric and Developmental Pathology , bind 11, nr. 1, s. 59-62. (regionh.dk)
Many of us directory a 1-week aged young lady using a pseudo-cor triatriatum dexter as well as instant cyanosis following a hassle-free delivery. (cdk-receptor.com)
Cor triatriatum represents 0.1% of all congenital cardiac malformations and may be associated with other cardiac defects in as many as 50% of cases. (wikipedia.org)
Prof Andrew Cook leads the Centre for Cardiac Morphology & Structural Heart Disease at UCL's Institute of Cardiovascular Science / Great Ormond Street Hospital, now based at the GOSH/UCL Zayed Centre for Research into Rare Disease in Children in central London, UK. (cardiacmorphology.com)
Cardiac transplantation in children with Noonan syndrome. (jefferson.edu)
Congenital heart d2
Transoesophageal echocardiographic evaluation of atrial morphology in children with congenital heart disease. (wikipedia.org)
[8] 45% of children with Down syndrome have congenital heart disease. (wikipedia.org)
Frontal Hypoactivation During a Working Memory Task in Children With 22q11 Deletion Syndrome. (harvard.edu)
Diagnosis and Management of Opsoclonus-Myoclonus-Ataxia Syndrome in Children: An International Perspective. (nih.gov)
Echocardiographic1
Diagnostic features and pitfalls in the two-dimensional echocardiographic evaluation of a child with cor triatriatum. (wikipedia.org)
Severe1
Abstract Successful airway management of an infant or child with moderate to severe retrognathia first requires recognition of a potential problem. (the-medical-dictionary.com)
Echocardiography1
This malformation has been diagnosed in adults and children by echocardiography, surgery, or autopsy but has not previously been published in fetuses. (regionh.dk)
Left3
Cor triatriatum (subdivided left atrium). (wikipedia.org)
The significance of a prominent or persistent left superior vena cava in the pathogenesis of cor triatriatum is unclear. (medscape.com)
The hearts described on the basis of "cor triatriatum", nonetheless, can also be analysed on the basis of division of either the morphologically right or the morphologically left atriums. (cambridge.org)
Own to the improvement in surgery intervention, women who suffer from congenital heart anomalies are more likely to live to the age of child-bearing (Gianopoulos 1989 ). (springeropen.com)
The purpose of this study was to determine whether antioxidant vitamin therapy improves endothelial function and affects surrogate biomarkers for oxidative stress and inflammation in hyperlipidemic children. (the-medical-dictionary.com)
Results1
METHODS AND RESULTS: In a randomized, double-blind, placebo-controlled trial, the effects of antioxidant vitamins C (500 mg/d) and E (400 IU/d) for 6 weeks and the National Cholesterol Education Program Step II (NCEP-II) diet for 6 months on endothelium-dependent flow-mediated dilation (FMD) of the brachial artery were examined in 15 children with familial hypercholesterolemia (FH) or the phenotype of familial combined hyperlipidemia (FCH). (the-medical-dictionary.com)
Division1
We then show how it is, indeed, the case that the hearts described in terms of "cor triatriatum" can be readily understood on the basis of division of these atrial components. (cambridge.org)
Parents1
Healthy living for parents, kids and teens. (nemours.org)