Cystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorFibrosisPseudomonas InfectionsPseudomonas aeruginosaSweatSputumChild WelfareMice, Inbred CFTRDisabled ChildrenChild BehaviorBurkholderia InfectionsBurkholderia cepaciaChloridesEndomyocardial FibrosisIdiopathic Pulmonary FibrosisLungExocrine Pancreatic InsufficiencyLiver CirrhosisChloride ChannelsNeonatal ScreeningRespiratory MucosaNasal MucosaTobramycinForced Expiratory VolumePancreatinRespiratory Function TestsRetroperitoneal FibrosisChild Health ServicesBurkholderia cepacia complexChild RearingRespiratory SystemBronchiectasisPancreatic ExtractsMutationLung DiseasesAnti-Bacterial AgentsChild, InstitutionalizedChild Behavior DisordersChild PsychologyEpithelial CellsParentsBronchiChild of Impaired ParentsLung TransplantationInfant, NewbornMucusHeterozygote DetectionMeconiumDental Care for ChildrenExpectorantsChild, OrphanedTime FactorsAlginatesChild Nutrition DisordersBleomycinPancrelipaseAge FactorsChild Nutritional Physiological PhenomenaTracheaGenotypeSeverity of Illness IndexAchromobacter denitrificansRetrospective StudiesTreatment OutcomeMucociliary ClearanceProspective StudiesPhenotypeDisease Models, AnimalSweat GlandsBurkholderia cenocepaciaChronic DiseaseCross-Sectional StudiesVital CapacityChild LanguagePrevalenceNutritional StatusAdministration, InhalationAminophenolsAspergillosis, Allergic BronchopulmonaryLeukocyte ElastaseIon TransportCase-Control StudiesGenetic TestingOral Submucous FibrosisCell LineFollow-Up StudiesChild MortalityRisk FactorsRespiratory Tract InfectionsLiver Cirrhosis, ExperimentalEpitheliumAmiloridePolymerase Chain ReactionCells, CulturedMothersBody HeightQuestionnairesMolecular Sequence DataDrainage, Postural