Cystic Fibrosis Transmembrane Conductance RegulatorMice, Inbred CFTRMembrane ProteinsMolecular Sequence DataAmino Acid SequenceCell MembraneProtein Structure, TertiaryMutationProtein Structure, SecondaryChloridesCell LineChloride ChannelsModels, MolecularMutagenesis, Site-DirectedBase SequenceSequence Homology, Amino AcidRecombinant Fusion ProteinsProtein ConformationProtein BindingTransfectionCricetinaeBinding SitesProtein TransportIon Channel GatingCOS CellsBiological TransportCloning, MolecularEndoplasmic ReticulumMembrane PotentialsIon TransportCHO CellsRecombinant ProteinsAmino Acid SubstitutionCysteineSignal TransductionEpithelial CellsLipid BilayersStructure-Activity RelationshipSequence AlignmentDNA, ComplementaryMembrane GlycoproteinsKineticsCytoplasmCyclic AMPXenopus laevisMembrane Transport ProteinsCystic FibrosisDimerizationProtein FoldingOocytesCells, CulturedRespiratory MucosaAdenosine TriphosphateCarrier ProteinsAmino Acid MotifsModels, BiologicalSequence DeletionPatch-Clamp TechniquesMutagenesisColforsinAminophenolsIodidesMesylatesRNA, MessengerAntiportersGlycosylationLigandsBiotinylationXenopusAnionsIntracellular MembranesHydrogen-Ion ConcentrationHydrophobic and Hydrophilic InteractionsReceptors, Cell SurfacePeptidesPoint MutationGene ExpressionCercopithecus aethiopsBicarbonatesEscherichia coliHEK293 CellsBacterial ProteinsNasal MucosaPhosphorylationIon ChannelsDNA PrimersEscherichia coli ProteinsProtein Processing, Post-TranslationalThiazolidinesProtein Multimerizationortho-AminobenzoatesElectrophysiologyProtein Sorting SignalsElectric ConductivityGolgi ApparatusCyclic AMP-Dependent Protein KinasesHeLa CellsMicroscopy, FluorescencePeptide FragmentsMutant Proteins