Mice, Inbred CFTRCystic Fibrosis Transmembrane Conductance RegulatorMice, TransgenicCystic FibrosisChloridesRespiratory MucosaChloride ChannelsMutationColforsinEpithelial CellsCell LineCyclic AMPMembrane ProteinsCricetinaeGene ExpressionLungRNA, MessengerMolecular Sequence DataCells, CulturedAminophenolsIodidesIon TransportThiazolidinesIon Channel GatingNasal MucosaSweat GlandsBicarbonatesortho-AminobenzoatesVas DeferensCyclic AMP-Dependent Protein KinasesEpithelial Sodium ChannelsCell Membrane