Cystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorFibrosisMice, Inbred CFTRSweatVas DeferensPseudomonas InfectionsChloridesMutationPseudomonas aeruginosaNasal MucosaChloride ChannelsSputumLungGenes, ModifierBurkholderia InfectionsBurkholderia cepaciaNeonatal ScreeningEpithelial CellsDNA Mutational AnalysisRespiratory MucosaEndomyocardial FibrosisIdiopathic Pulmonary FibrosisIon TransportGenetic TestingHeterozygoteGenotypeExocrine Pancreatic InsufficiencyExonsPhenotypeEchogenic BowelUrogenital AbnormalitiesLiver CirrhosisCell LineTobramycinInfertility, MaleGenetic CounselingBase SequencePancreatinRespiratory SystemForced Expiratory VolumeMolecular Sequence DataAllelesColforsinRetroperitoneal FibrosisHomozygoteMembrane ProteinsBurkholderia cepacia complexBronchiBronchiectasisPolymerase Chain ReactionRespiratory Function TestsEpitheliumChromosomes, Artificial, YeastPancreatic ExtractsRNA, MessengerCyclic AMPAminophenolsLung DiseasesGenetic TherapySweat GlandsIntronsDeoxyribonuclease IMucusCells, CulturedTracheaGene ExpressionLung TransplantationHeterozygote DetectionSequence DeletionAnti-Bacterial AgentsMeconiumExpectorantsAlginatesPoint MutationMucociliary ClearanceMutation, MissenseBleomycinPancrelipaseAmilorideGene Expression RegulationPolymorphism, GeneticIodidesDisease Models, AnimalAchromobacter denitrificansBurkholderia cenocepaciaInfant, NewbornBicarbonatesGene FrequencyOligospermiaAspergillosis, Allergic BronchopulmonaryPancreatitisTransfectionortho-AminobenzoatesLeukocyte ElastaseOral Submucous FibrosisHaplotypesVital CapacityRespiratory Tract InfectionsEpithelial Sodium Channels