CeruloplasminHepatolenticular DegenerationCopperCation Transport ProteinsMenkes Kinky Hair SyndromeAdenosine TriphosphatasesRats, Inbred LECMetallochaperonesTrientinePenicillamineExtrapyramidal TractsChelating AgentsChelation TherapyRats, Mutant StrainsChromosomes, Human, Pair 13Iron Metabolism DisordersCarrier ProteinsIronLiverMutationCarboxylesteraseMetal Metabolism, Inborn ErrorsMolecular Sequence DataZincBase SequenceAmino Acid SequenceTransferrinDNA Mutational AnalysisMutation, MissenseLymphangiectasisLiver Function TestsHepatocytesDNA PrimersGolgi ApparatusDisease Models, AnimalGenetic MarkersDeficiency DiseasesTurpentineBiological TransportDNA, ComplementaryAnserineHaptoglobinsHomozygoteModels, MolecularRecombinant Fusion ProteinsPhenotypeProtein Structure, TertiaryKineticsPedigree