Wegener GranulomatosisLymphomatoid GranulomatosisAntibodies, Antineutrophil CytoplasmicMyeloblastinVasculitisMicroscopic PolyangiitisGranulomatosis, OrofacialChurg-Strauss SyndromeAnti-Neutrophil Cytoplasmic Antibody-Associated VasculitisCarbenoxoloneReceptors, CCRPolyarteritis NodosaSerine EndopeptidasesHistiocytosis, Langerhans-CellSarcoidosisGranulomaScleritisImmunosuppressive AgentsCryopyrin-Associated Periodic SyndromesNose Deformities, AcquiredLung DiseasesAutoantibodiesVasculitis, Leukocytoclastic, CutaneousIleitisBronchial DiseasesLaryngostenosisGlomerulonephritisCyclophosphamideArteritisPrednisoloneSyndromeFluorescent Antibody Technique, IndirectAutoantigensBehcet SyndromePeroxidaseSarcoidosis, PulmonaryOrbital DiseasesBiopsyNeutrophilsEosinophilic GranulomaNose DiseasesSkin DiseasesGranuloma, Respiratory TractFatal OutcomeSystemic VasculitisRecurrenceGranuloma, Lethal MidlinePseudoxanthoma ElasticumLip DiseasesEndpoint DeterminationTreatment OutcomeEnzyme-Linked Immunosorbent AssayImmunoglobulin GCathepsin GNeutrophil ActivationTomography, X-Ray ComputedAllostasisCrohn DiseaseAutoimmune DiseasesAntibodies, Monoclonal, Murine-DerivedRemission InductionMyotonic DisordersLeukocyte ElastaseSkin Diseases, VascularEye DiseasesPurpura, Schoenlein-HenochCranial Nerve DiseasesMethylprednisoloneIleal DiseasesMyotonic DystrophySkin ManifestationsAlagille SyndromeMultiple TraumaPrednisonePlasma ExchangeAzathioprineFocal Dermal HypoplasiaRetrospective StudiesHorner SyndromeGlycogen Storage Disease Type IIbEndoscopy, GastrointestinalOtorhinolaryngologic DiseasesGlucocorticoidsOphthalmoplegiaBiological MarkersFacial ParalysisTalcHobbiesKidneys, ArtificialAdrenal Cortex HormonesLymphangioleiomyomatosisCongenital Disorders of GlycosylationMouth DiseasesDe Lange SyndromeLupus Erythematosus, SystemicTuberous Sclerosis