ArylsulfatasesCerebroside-SulfataseSulfatasesChondro-4-SulfataseLeukodystrophy, MetachromaticN-Acetylgalactosamine-4-SulfataseMucopolysaccharidosis VISteryl-SulfataseTyramineSulfoglycosphingolipidsSulfatesMucopolysaccharidosesMucopolysaccharidosis IVLysosomesVitamin A DeficiencySaposinsDeficiency DiseasesKlebsiellaSphingolipid Activator Proteinsalpha 1-Antitrypsin DeficiencyPhotofluorographyDiazomethaneEnzyme RepressionVitamin B 12 DeficiencyMolecular Sequence DataGalactolipidsMonoamine OxidaseVitamin D DeficiencyMutationFolic Acid DeficiencyIgA DeficiencyThiamine DeficiencyChondrodysplasia PunctataSulfurAutacoidsBase SequenceMycobacterium scrofulaceumGlucosephosphate Dehydrogenase DeficiencyCitrobacterFibroblastsMagnesium DeficiencyAnemia, Iron-DeficiencyVitamin E DeficiencyImmunochemistryAmino Acid SequenceLiverAscorbic Acid DeficiencyMice, KnockoutLysosomal Storage DiseasesImmunologic Deficiency SyndromesEnzyme Replacement TherapyTransferases (Other Substituted Phosphate Groups)Acid PhosphataseCathepsin DProtein C DeficiencyGenesAmmonium ChlorideIgG DeficiencyHomozygotePhenotypeCloning, MolecularNitrosoguanidinesVitamin B 6 DeficiencyMethionineAllelesMannosyl-Glycoprotein Endo-beta-N-AcetylglucosaminidasePedigreeHydrogen-Ion ConcentrationIsoelectric FocusingRestriction MappingFactor V DeficiencyImmunodiffusionCells, CulturedIronOligosaccharidesSRS-ARiboflavin DeficiencyImmunoelectrophoresis, Two-DimensionalGlycosylationChlorophytaTryptaminesMycobacteriumElectrophoresis, Polyacrylamide GelAntithrombin III DeficiencyChromatography, Ion ExchangeChemistryGlucuronidaseKlebsiella pneumoniaeDisease Models, AnimalChemical PhenomenaMice, Inbred C57BLCell LineKineticsMetabolism, Inborn ErrorsChlamydomonas reinhardtiiHydrolasesMycolic AcidsGenes, RegulatorEnterobacterRNA, Messenger