Muscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinAtrophySMN Complex ProteinsMuscular AtrophySurvival of Motor Neuron 2 ProteinSpinal CordMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedBrain StemSpinal Cord InjuriesNeuronal Apoptosis-Inhibitory ProteinMotor NeuronsCyclic AMP Response Element-Binding ProteinAnterior Horn CellsRNA-Binding ProteinsNerve Tissue ProteinsSpinal Cord DiseasesEvoked Potentials, Auditory, Brain StemOptic AtrophyMotor Neuron DiseaseRibonucleoproteins, Small NuclearDEAD Box Protein 20Disease Models, AnimalSpinal Nerve RootsChromosomes, Human, Pair 5Injections, SpinalExonsSpinal NervesMultiple System AtrophyCoiled BodiesAnesthesia, SpinalBrain Stem NeoplasmsReceptors, AndrogensnRNP Core ProteinsSpinal Cord NeoplasmsSpinal CanalMagnetic Resonance ImagingMuscle, SkeletalSpinal DiseasesSpinal Cord CompressionElectromyographyMice, TransgenicSpinal NeoplasmsPedigreeBulbar Palsy, ProgressiveSpinal StenosisNerve DegenerationAxonsSpinal FusionOlivopontocerebellar AtrophiesPhenotypeNeuronsCharcot-Marie-Tooth DiseaseBrainMuscle WeaknessHeterozygote DetectionNeural ConductionContracturePonsNeuromuscular DiseasesGlycine-tRNA LigaseArthrogryposisGene DeletionVocal Cord ParalysisMutationHomozygoteSpinal InjuriesGyrate AtrophyAmyotrophic Lateral SclerosisRats, Sprague-DawleyNeuromuscular JunctionTrinucleotide Repeat ExpansionNeuromuscular Junction DiseasesRNA SplicingGanglia, SpinalSpinal Cord IschemiaGenes, RecessiveMotor ActivitySural NerveGeographic AtrophyGenetic LinkageGene DosageTrinucleotide RepeatsAuditory PathwaysMedulla OblongataTime FactorsAnimals, NewbornImmunohistochemistryInclusion BodiesIntranuclear Inclusion BodiesGenes, DominantMyelographyParaplegiaFasciculationMyoclonic Epilepsies, ProgressiveChemistry, AnalyticSpineBrain Stem Infarctions