GangliosidosesLipidosesHexosaminidase AHexosaminidase BHexosaminidasesbeta-N-AcetylhexosaminidasesTay-Sachs DiseaseG(M2) GangliosideSandhoff DiseaseProtein SubunitsG(M2) Activator ProteinAcetylglucosaminidaseInterleukin-1betaMacromolecular SubstancesMolecular Sequence DataAmino Acid SequenceChromosomes, Human, 4-5IsoenzymesSphingolipid Activator Proteinsbeta 2-MicroglobulinKineticsBase SequenceHymecromoneGangliosidoses, GM2Integrin beta3Receptors, Adrenergic, betaProtein ConformationMolecular WeightCell LineElectrophoresis, Polyacrylamide GelLarge-Conductance Calcium-Activated Potassium Channel beta SubunitsIntegrin alpha5beta1IntegrinsMutationRecombinant ProteinsSaposinsChromosomes, Human, 13-15Binding SitesCloning, MolecularElectrophoresis, Starch GelIntegrin alpha4beta1AcetylglucosamineIntegrin alpha6beta4Cells, CulturedLysosomesIntegrin alpha2beta1RNA, MessengerTransforming Growth Factor betaTransfectionIsoelectric FocusingHeterozygote DetectionSubstrate SpecificitySequence Homology, Amino Acidalpha 1-AntitrypsinIntegrin beta ChainsIntegrin alpha6beta1Protein BindingIntegrin alpha1beta1Signal TransductionProton-Translocating ATPasesFibroblastsHot TemperatureIntegrin beta4LiverChromatography, Ion ExchangeModels, MolecularHypoxia-Inducible Factor 1, alpha SubunitGTP-Binding ProteinsChromatography, GelPeptide FragmentsGTP-Binding Protein beta SubunitsCattleAntigens, CD29Gene Expression RegulationGene ExpressionRecombinant Fusion ProteinsPhosphorylationGangliosides