Amino Acids, Branched-ChainAmino AcidsSequence Homology, Amino AcidTransaminasesLeucineIsoleucine3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)Maple Syrup Urine DiseaseAmino Acid SequenceAmino Acid SubstitutionCloning, MolecularAmmoniaPolymerase Chain ReactionAmino Acids, EssentialBase SequenceMolecular Sequence DataAmino Acid Transport SystemsSequence AlignmentMutationEscherichia coliBinding SitesAmino Acid MotifsKineticsProtein ConformationPeptide FragmentsDNA, ComplementaryModels, MolecularSequence Homology, Nucleic AcidMuscle, SkeletalRecombinant ProteinsMutagenesis, Site-DirectedAmino Acids, AromaticMolecular WeightProtein BindingProtein Structure, TertiaryDNAAmino Acids, SulfurPeptidesSubstrate SpecificityRNA, MessengerCell LineBacterial ProteinsElectrophoresis, Polyacrylamide GelStructure-Activity RelationshipRestriction MappingImmunoglobulin Light ChainsPhylogenySequence Analysis, DNARecombinant Fusion ProteinsDNA PrimersProteinsProtein Structure, SecondaryAlanineImmunoglobulin Heavy ChainsGenes, BacterialChromatography, High Pressure LiquidCattleSpecies SpecificityLysineConserved SequenceCarrier ProteinsAmino Acid Transport Systems, BasicCyanogen BromideTrypsinMacromolecular SubstancesPlasmidsCodonGenesAmino Acids, BasicReverse Transcriptase Polymerase Chain ReactionBiological TransportProtein BiosynthesisGlycineGene LibraryGlutaminePoint MutationMethionineTransfectionArginineValineSaccharomyces cerevisiaeTranscription, GeneticGene ExpressionMembrane ProteinsOpen Reading FramesSequence DeletionAmino Acids, DiaminoAspartic AcidSequence AnalysisMutagenesisProlineCysteineDNA, BacterialPhenylalanineRabbitsMyosin Heavy ChainsExcitatory Amino AcidsBlotting, NorthernNitrogenTryptophan