AztreonamCystic FibrosisLysineCystic Fibrosis Transmembrane Conductance RegulatorFibrosisMonobactamsPseudomonas InfectionsPseudomonas aeruginosaAnti-Bacterial Agentsbeta-LactamasesCeftazidimeMicrobial Sensitivity TestsSweatSputumbeta-LactamsTobramycinMice, Inbred CFTRCephalosporinsBurkholderia InfectionsBurkholderia cepaciaChloridesEndomyocardial FibrosisIdiopathic Pulmonary FibrosisLungMutationExocrine Pancreatic InsufficiencyMolecular Sequence Databeta-Lactam ResistanceLiver CirrhosisChloride ChannelsGram-Negative BacteriaAzlocillin