Motor NeuronsAstrocytesNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateSpinal CordEvoked Potentials, MotorAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalMotor ActivityCells, CulturedAxonsNerve Tissue ProteinsGlial Fibrillary Acidic ProteinSMN Complex ProteinsAction PotentialsTime FactorsImmunohistochemistryBrainDisease-Free SurvivalMice, TransgenicAnimals, NewbornNerve DegenerationNeurogliaSurvivalSynapsesCerebral CortexElectric StimulationMolecular Motor ProteinsDisease Models, AnimalNeuromuscular DiseasesMice, Inbred C57BLGanglia, InvertebrateSynaptic TransmissionElectrophysiologySurvival AnalysisGlutamic AcidHippocampusInterneuronsSuperoxide DismutaseRats, Sprague-DawleyGraft SurvivalCholinergic NeuronsSignal TransductionDopaminergic NeuronsMovementPatch-Clamp TechniquesAplysiaDendritesAnterior Horn CellsGanglia, SpinalMutationCentral Nervous SystemElectromyographyMice, KnockoutSensory Receptor CellsNeuromuscular JunctionModels, NeurologicalCell DifferentiationNeural InhibitionCell CountGABAergic NeuronsBulbar Palsy, ProgressiveMembrane PotentialsGliosisGreen Fluorescent ProteinsRats, WistarCell Deathgamma-Aminobutyric AcidAnimals, Genetically ModifiedAnalysis of VarianceNerve Growth FactorsNeuropeptidesFacial NerveBrain StemRNA, MessengerCerebellumMotor Skills DisordersApoptosisGene Expression Regulation, DevelopmentalNeurofilament ProteinsBehavior, AnimalAxonal TransportOligodendrogliaNeuronal PlasticityNeurogenesisNerve NetTreatment OutcomeCholine O-AcetyltransferaseExcitatory Postsynaptic PotentialsMicrogliaLocomotionCalciumGene Expression RegulationNeural Conduction