PrPSc ProteinsPrion DiseasesPrionsPrPC ProteinsCreutzfeldt-Jakob SyndromeGerstmann-Straussler-Scheinker DiseaseEndopeptidase KInsomnia, Fatal FamilialScrapieEncephalopathy, Bovine SpongiformAmyloidKuruProtein FoldingWasting Disease, ChronicBrainProtein Structure, SecondaryProtein ConformationPeptide FragmentsNuclear Magnetic Resonance, BiomolecularMice, TransgenicInfectious Disease Incubation PeriodMutationCircular DichroismDeerModels, MolecularMolecular Sequence DataRecombinant ProteinsSheepAmino Acid SequenceCodonMesocricetusCattleMutant ProteinsCricetinaeProtein Structure, TertiaryPrP 27-30 ProteinMagnetic Resonance SpectroscopyBlotting, WesternCopperMethioninePolymorphism, GeneticProtein IsoformsHydrogen-Ion ConcentrationImmunohistochemistryProtein BindingGlycosylationDisease Models, AnimalPhenotypeRNA, MessengerMice, Inbred C57BLNeuronsBrain ChemistryCells, CulturedTime FactorsGlycosylphosphatidylinositolsCell LineNeurodegenerative DiseasesDendritic Cells, FollicularProteostasis DeficienciesValineTumor Suppressor Protein p53Repetitive Sequences, Amino AcidQuinacrineRuminantsSpecies SpecificityPentosan Sulfuric PolyesterBentoniteAmyloidogenic ProteinsProtein TransportPlant ProteinsNeuroblastomaGPI-Linked ProteinsMice, KnockoutPeptidesAmino Acid SubstitutionBase SequenceKineticsLibyaProtein DenaturationImmunoblottingGene Expression Regulation, PlantModels, BiologicalPlants, Genetically ModifiedRecombinant Fusion ProteinsCell Line, TumorNerve DegenerationDetergentsGoatsProteasome Endopeptidase ComplexProtein Structure, Quaternary