PrPSc ProteinsPrion DiseasesPrionsPrPC ProteinsCreutzfeldt-Jakob SyndromeGerstmann-Straussler-Scheinker DiseaseEndopeptidase KScrapieEncephalopathy, Bovine SpongiformInsomnia, Fatal FamilialAmyloidKuruProtein FoldingWasting Disease, ChronicBrainProtein Structure, SecondaryProtein ConformationPeptide FragmentsNuclear Magnetic Resonance, BiomolecularMice, TransgenicPuerperal DisordersDeerMutationModels, MolecularCircular DichroismMolecular Sequence DataSheepRecombinant ProteinsAmino Acid SequenceMesocricetusCricetinaeCodonCattleProtein Structure, TertiaryMutant ProteinsPrP 27-30 ProteinMagnetic Resonance SpectroscopyBlotting, WesternCopperMethioninePolymorphism, GeneticProtein IsoformsHydrogen-Ion ConcentrationImmunohistochemistryProtein BindingGlycosylationDisease Models, AnimalMice, Inbred C57BLPhenotypeNeuronsBrain ChemistryRNA, MessengerTime FactorsDendritic Cells, FollicularGlycosylphosphatidylinositolsCells, CulturedNeurodegenerative DiseasesProteostasis DeficienciesCell LineRepetitive Sequences, Amino AcidSpecies SpecificityRuminantsAmyloidogenic ProteinsBentoniteValineQuinacrinePentosan Sulfuric PolyesterTumor Suppressor Protein p53GPI-Linked ProteinsNeuroblastomaKineticsBase SequenceProtein TransportPeptidesMice, KnockoutSaccharomyces cerevisiae ProteinsLibyaProtein DenaturationAmino Acid SubstitutionPlant ProteinsImmunoblottingModels, BiologicalCell Line, TumorProtein Structure, QuaternaryRecombinant Fusion ProteinsDetergentsGoatsNerve DegenerationSpectroscopy, Fourier Transform InfraredCongo RedGene Expression Regulation, PlantSheep DiseasesPlants, Genetically ModifiedProteasome Endopeptidase ComplexCell MembraneDisease SusceptibilityGene Expression RegulationEndoplasmic ReticulumBiological AssaySaccharomyces cerevisiae