Amyotrophic Lateral SclerosisMultiple SclerosisSclerosisSuperoxide DismutaseTuberous SclerosisMotor Neuron DiseaseMotor NeuronsScleroderma, SystemicRNA-Binding Protein FUSSpinal CordDNA Repeat ExpansionMultiple Sclerosis, Chronic ProgressiveFrontotemporal DementiaGuamRiluzoleMice, TransgenicInclusion BodiesFrontotemporal Lobar DegenerationDisease Models, AnimalNerve DegenerationNeurodegenerative DiseasesMutationBrainDisease ProgressionFasciculationTDP-43 ProteinopathiesAnterior Horn CellsNeurofilament ProteinsMagnetic Resonance ImagingBulbar Palsy, ProgressiveAge of OnsetEncephalomyelitis, Autoimmune, ExperimentalScleroderma, DiffuseAstrocytesMicrogliaDemyelinating DiseasesDiffuse Cerebral Sclerosis of SchilderRats, TransgenicCase-Control StudiesAxonsNeuroprotective AgentsCycasAtrophyMutation, MissenseOptic NeuritisCentral Nervous SystemScleroderma, LimitedNeuronsLithium CarbonateDNA-Binding ProteinsPyramidal TractsExcitatory Amino Acid Transporter 2Myelin Basic ProteinRotarod Performance TestMutant ProteinsPseudobulbar PalsyDisability EvaluationAmino Acid SubstitutionMice, Inbred C57BLSialorrheaOligoclonal BandsAxonal TransportInterferon-betaMyelin SheathPhenotypeNoninvasive VentilationNeuromuscular DiseasesGenetic Predisposition to DiseaseNervous System DiseasesRibonuclease, PancreaticMyelin-Oligodendrocyte GlycoproteinCell DeathRaynaud DiseaseMitochondriaMuscle WeaknessImmunohistochemistryNerve Fibers, MyelinatedAnimals, Genetically ModifiedAngiomyolipomaGlial Fibrillary Acidic ProteinAmino Acids, DiaminoNeurogliaCells, CulturedPeritoneal FibrosisSeverity of Illness IndexPedigreeElectromyographyLaughterTime FactorsItalyEpilepsy, Temporal LobePeripherinsNerve Tissue ProteinsProtein FoldingScleroderma, LocalizedDementiaGliosisParalysisMyelin ProteinsCopper