Amyotrophic Lateral SclerosisMuscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinAtrophySpinal CordSMN Complex ProteinsMuscular AtrophySurvival of Motor Neuron 2 ProteinMotor NeuronsMotor Neuron DiseaseSuperoxide DismutaseAnterior Horn CellsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesRNA-Binding Protein FUSNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinDisease Models, AnimalMice, TransgenicDNA Repeat ExpansionInclusion BodiesRNA-Binding ProteinsNerve Tissue ProteinsNerve DegenerationFrontotemporal DementiaMutationRiluzoleGuamFrontotemporal Lobar DegenerationBulbar Palsy, ProgressiveFasciculationNeurodegenerative DiseasesSpinal Cord DiseasesOptic AtrophyRibonucleoproteins, Small NuclearNeurofilament ProteinsExonsSpinal Nerve RootsMuscle, SkeletalInjections, SpinalAxonsDEAD Box Protein 20TDP-43 ProteinopathiesDisease ProgressionPedigreeBrainMuscle WeaknessNeuromuscular DiseasesMultiple System AtrophyNeuronsElectromyographyPhenotypeChromosomes, Human, Pair 5Mutation, MissenseMagnetic Resonance ImagingAge of OnsetSpinal NervesNeuromuscular JunctionRotarod Performance TestCoiled BodiesAnesthesia, SpinalNeuroprotective AgentsReceptors, AndrogensnRNP Core ProteinsNeural ConductionSpinal CanalRats, TransgenicSpinal Cord NeoplasmsMutant ProteinsSpinal Cord CompressionSpinal DiseasesDNA-Binding ProteinsAstrocytesSpinal NeoplasmsPyramidal TractsCycasIntranuclear Inclusion BodiesMotor ActivityAnimals, Genetically ModifiedMicrogliaImmunohistochemistrySpinal FusionTime FactorsLithium CarbonateSpinal StenosisHomozygoteExcitatory Amino Acid Transporter 2Mice, Inbred C57BLCentral Nervous SystemGenes, DominantAxonal TransportMolecular Sequence DataGene DeletionTrinucleotide Repeat ExpansionParalysisCharcot-Marie-Tooth DiseaseHeterozygote DetectionContracture