Cryopyrin-Associated Periodic SyndromesAmyloidosisFamilial Mediterranean FeverHereditary Autoinflammatory DiseasesReceptors, Tumor Necrosis Factor, Type ISyndromeAmyloidosis, FamilialSchnitzler SyndromeSerum Amyloid A ProteinMevalonate Kinase DeficiencyCaspase 1Interleukin-1betaReceptors, Tumor Necrosis FactorCarrier ProteinsHearing Loss, Mixed Conductive-SensorineuralMutationInterleukin 1 Receptor Antagonist ProteinHypergammaglobulinemiaPenetranceAmyloidArthritis, GoutyPrealbuminPedigreeDNA Mutational AnalysisCytoskeletal ProteinsNephrotic SyndromeJoint DiseasesImmunoglobulin Light ChainsAntigens, CDInflammationDermatitisAmyloid NeuropathiesDown SyndromeMetabolic Syndrome XInterleukin-18Congo RedAmyloid Neuropathies, FamilialMacrophagesCardiomyopathiesSjogren's SyndromeConnexinsbeta 2-MicroglobulinSerum Amyloid P-ComponentKidney DiseasesEnzyme ActivationParaproteinemiasTracheal DiseasesMice, KnockoutMacroglossiaBiopsyAmyloidogenic ProteinsTurner SyndromeFatal Outcome