Motor NeuronsMuscular Atrophy, SpinalSurvival of Motor Neuron 1 ProteinSurvival of Motor Neuron 2 ProteinSMN Complex ProteinsNeuronsMotor Neuron DiseaseCyclic AMP Response Element-Binding ProteinRNA-Binding ProteinsNerve Tissue ProteinsSpinal Muscular Atrophies of ChildhoodRibonucleoproteins, Small NuclearCoiled BodiesDEAD Box Protein 20Spinal CordNeurons, AfferentCell SurvivalMotor CortexSurvival RateEvoked Potentials, MotorMolecular Sequence DataAmyotrophic Lateral SclerosisExonsMotor ActivityAmino Acid SequenceCells, CulturedDisease Models, AnimalMutationAxonsMice, TransgenicImmunohistochemistryTime FactorsBase SequenceAlternative SplicingAction PotentialsCell LineSpliceosomesHeLa CellsDisease-Free SurvivalRNA SplicingBlotting, WesternFibroblastsSurvivalRNA, MessengerElectric StimulationMolecular Motor ProteinsCloning, MolecularNerve DegenerationSynapsesSmall Molecule LibrariesSurvival AnalysisProtein BindingNeuromuscular DiseasesGanglia, InvertebrateElectrophysiologyBrainCholinergic NeuronsInterneuronsSynaptic TransmissionMovementTranscription, GeneticMice, Inbred C57BLGraft SurvivalNeuromuscular JunctionSuperoxide DismutaseElectromyographyAnimals, NewbornSignal TransductionAplysiaAnterior Horn CellsDopaminergic NeuronsPrecipitin TestsDendritesLength of StaySensory Receptor CellsDNA, ComplementaryGanglia, SpinalPatch-Clamp TechniquesModels, NeurologicalNeural InhibitionGreen Fluorescent ProteinsBulbar Palsy, ProgressiveGABAergic NeuronsGene ExpressionTreatment OutcomeMuscle, SkeletalCerebral CortexAnimals, Genetically ModifiedCell DifferentiationDNAMice, KnockoutHippocampusMembrane PotentialsGene Expression Regulation, DevelopmentalGene Expression RegulationAnalysis of VariancePhenotypeCell CountApoptosisFacial Nerve