CystineAmino AcidsSequence Homology, Amino AcidAmino Acid SequenceAmino Acid SubstitutionCystinosisAbsorptionCloning, MolecularAmino Acids, EssentialAmino Acid Transport SystemsKidney Tubules, ProximalAmino Acids, SulfurSequence AlignmentBase SequenceKidney TubulesCystine Knot MotifsMolecular Sequence DataMutationAmino Acid MotifsKineticsEscherichia coliSodiumAmino Acid Transport System y+Binding SitesKidney Tubules, DistalKidneyMutagenesis, Site-DirectedAmino Acid Transport Systems, BasicDNA, ComplementaryBiological TransportCystinuriaCysteinePeptide FragmentsProtein ConformationRecombinant ProteinsModels, MolecularLeucineAmino Acids, AromaticAmino Acids, Branched-ChainSequence Homology, Nucleic AcidStructure-Activity RelationshipProtein Structure, TertiaryPeptidesMolecular WeightProtein BindingSubstrate SpecificityCell LineMethionineDNACarrier ProteinsNephronsBacterial ProteinsProteinsRNA, MessengerHydrogen-Ion ConcentrationCysteamineInulinAlanineRestriction MappingPhylogenyElectrophoresis, Polyacrylamide GelChromatography, High Pressure LiquidBicarbonatesAmino Acids, DiaminoLysineLoop of HenleSequence Analysis, DNARecombinant Fusion ProteinsFanconi SyndromeProtein Structure, SecondaryGlomerular Filtration RateGenes, BacterialSpecies SpecificityConserved SequenceAmino Acids, NeutralDNA PrimersCattleAmino Acid Transport Systems, NeutralPlasmidsIsoleucineArginineBiological Transport, ActiveTrypsinNatriuresisAmino Acids, BasicGlycineDisulfidesCyanogen BromideDiuresisGlutamineRabbitsPuncturesCodonNitrogenSodium ChlorideWater-Electrolyte BalanceKidney Tubules, CollectingProlineMembrane ProteinsTryptophan