Motor NeuronsMotor Neuron DiseaseNeuronsSurvival of Motor Neuron 1 ProteinNeurons, AfferentMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalMotor ActivityAxonsSMN Complex ProteinsAction PotentialsNerve Tissue ProteinsElectric StimulationMolecular Motor ProteinsSynapsesNerve DegenerationNeuromuscular DiseasesElectrophysiologyGanglia, InvertebrateMice, TransgenicCells, CulturedSynaptic TransmissionInterneuronsalpha 1-AntitrypsinImmunohistochemistryMovementCholinergic NeuronsAplysiaPatch-Clamp TechniquesSuperoxide DismutaseDopaminergic NeuronsBrainTime FactorsElectromyographyNeuromuscular JunctionAnterior Horn CellsMutationDendritesSensory Receptor CellsNeural InhibitionGanglia, SpinalDisease Models, AnimalGABAergic NeuronsBulbar Palsy, ProgressiveAnimals, NewbornMice, Inbred C57BLModels, NeurologicalReceptors, Adrenergic, alphaCerebral CortexMembrane Potentialsgamma-Aminobutyric AcidHippocampusAnimals, Genetically ModifiedSignal TransductionFacial NerveMice, KnockoutHypoxia-Inducible Factor 1, alpha SubunitRats, Sprague-DawleyMolecular Sequence DataMotor Skills DisordersBrain StemNeuropeptidesMuscle, SkeletalAxonal TransportCell DifferentiationGene Expression Regulation, DevelopmentalNeural ConductionBehavior, AnimalCentral Nervous SystemCholine O-AcetyltransferaseGangliaLocomotionNeurons, EfferentNerve NetGrasshoppersRats, WistarNeurofilament ProteinsCell CountReaction TimeExcitatory Postsynaptic PotentialsGene Expression RegulationMedulla OblongataGlutamic AcidNeuronal PlasticityEvoked PotentialsTranscription FactorsGreen Fluorescent ProteinsCatsChick EmbryoBase SequenceMusclesDopaminePsychomotor Performancealpha7 Nicotinic Acetylcholine ReceptorOlfactory Receptor NeuronsAnalysis of Variance