Motor NeuronsMotor Neuron DiseaseNeuronsMusclesSurvival of Motor Neuron 1 ProteinNeurons, AfferentMuscle, SkeletalMotor CortexMuscle ProteinsEvoked Potentials, MotorSurvival of Motor Neuron 2 ProteinMuscle, SmoothSpinal CordAmyotrophic Lateral SclerosisMuscle ContractionMuscle Fibers, SkeletalMuscle, Smooth, VascularMotor ActivityMuscular Atrophy, SpinalMuscle DevelopmentAxonsAction PotentialsElectromyographyElectric StimulationSMN Complex ProteinsCells, CulturedNerve Tissue ProteinsMuscle DenervationMolecular Motor ProteinsTime FactorsMovementMuscle FatigueElectrophysiologyNeuromuscular DiseasesNeuromuscular JunctionMice, TransgenicImmunohistochemistrySynapsesMuscle Fibers, Fast-TwitchNerve DegenerationGanglia, InvertebrateSynaptic TransmissionMuscle Fibers, Slow-TwitchMutationMuscle SpindlesMice, Inbred C57BLSignal TransductionMyocytes, Smooth MuscleRats, Sprague-DawleyMolecular Sequence DataOculomotor MusclesMitochondria, MuscleInterneuronsMembrane PotentialsNeck MusclesDisease Models, AnimalPatch-Clamp Techniquesalpha 1-AntitrypsinSuperoxide DismutaseBrainAnimals, NewbornCalciumModels, BiologicalMuscle WeaknessMuscle, StriatedCholinergic NeuronsAplysiaRats, WistarMuscle RelaxationMice, KnockoutDopaminergic NeuronsSensory Receptor CellsNeural InhibitionMuscular AtrophyAnterior Horn CellsBiomechanical PhenomenaCell DifferentiationGene Expression RegulationDendritesGanglia, SpinalProtein BindingCatsRespiratory MusclesReceptors, Adrenergic, alphaBulbar Palsy, ProgressiveModels, NeurologicalRNA, MessengerBase SequenceGABAergic NeuronsLocomotionTranscription FactorsAnimals, Genetically ModifiedGene Expression Regulation, DevelopmentalCerebral CortexFacial MusclesNeural ConductionAmino Acid SequencePapillary MusclesFacial Nervegamma-Aminobutyric Acid