Digestive System NeoplasmsDigestive System DiseasesDigestive SystemCystic FibrosisDigestive System and Oral Physiological PhenomenaCystic Fibrosis Transmembrane Conductance RegulatorDigestive System Physiological PhenomenaDigestive System ProcessesFibrosisLungDigestive System FistulaGastrointestinal TractClemastineGastrointestinal NeoplasmsLung DiseasesDiagnostic Techniques, Digestive SystemDigestive System AbnormalitiesGastrointestinal DiseasesPseudomonas InfectionsPancreasPseudomonas aeruginosaIntestinesLung NeoplasmsStomachLarvaSputumLung TransplantationSweatMice, Inbred CFTRTissue DistributionBurkholderia InfectionsLung InjuryBurkholderia cepaciaMolecular Sequence DataIdiopathic Pulmonary FibrosisChloridesEndomyocardial FibrosisRespiratory MucosaExocrine Pancreatic InsufficiencyCause of DeathCarcinoma, Non-Small-Cell LungTime FactorsRespiratory Function TestsForced Expiratory VolumeLiver CirrhosisNeoplasmsTobramycinChloride ChannelsStomach NeoplasmsRisk FactorsEpithelial CellsPancreatinNasal MucosaGenetic Predisposition to DiseaseMutationBronchiAcute Lung InjuryLiver NeoplasmsChinaNeonatal ScreeningEndoscopy, Digestive SystemRetroperitoneal FibrosisPancreatic ExtractsPhylogenyAsian Continental Ancestry GroupBurkholderia cepacia complexRespiratory SystemPolymorphism, GeneticBronchiectasisAnti-Bacterial AgentsBleomycinMucusBronchoalveolar Lavage FluidLung Volume MeasurementsDigestive System Surgical ProceduresExpectorantsLung Diseases, InterstitialVital CapacityHeterozygote DetectionMeconiumMice, Inbred C57BLTrypsinogenAlginatesAdministration, InhalationEpitheliumDigestionCell LineNational Institute of Diabetes and Digestive and Kidney Diseases (U.S.)RNA, MessengerPulmonary AlveoliMucociliary ClearancePhenotypeTracheaPancrelipaseCells, CulturedAchromobacter denitrificansDisease Models, AnimalExocrine GlandsLeukocyte ElastaseBurkholderia cenocepacia