Cystic FibrosisSputumPseudomonas InfectionsPseudomonas aeruginosaRespiratory Function TestsForced Expiratory VolumeCystic Fibrosis Transmembrane Conductance RegulatorAnti-Bacterial AgentsBurkholderia cepaciaBurkholderia InfectionsExocrine Pancreatic InsufficiencyAchromobacter denitrificansBurkholderia cepacia complexNasal MucosaStenotrophomonas maltophiliaTobramycinBurkholderia cenocepacia