Amyotrophic Lateral SclerosisSuperoxide DismutaseMotor Neuron DiseaseMotor NeuronsRNA-Binding Protein FUSMultiple SclerosisSpinal CordDNA Repeat ExpansionFrontotemporal DementiaGuamRiluzoleFrontotemporal Lobar DegenerationInclusion BodiesMice, TransgenicNerve DegenerationDisease Models, AnimalNeurodegenerative DiseasesMutationFasciculationTDP-43 ProteinopathiesAnterior Horn CellsSclerosisBulbar Palsy, ProgressiveNeurofilament ProteinsDisease ProgressionRats, TransgenicBrainAge of OnsetTuberous SclerosisLithium CarbonateMutation, MissenseCycasAstrocytesNeuronsNeuroprotective AgentsExcitatory Amino Acid Transporter 2DNA-Binding ProteinsMicrogliaPyramidal TractsPseudobulbar PalsyMutant ProteinsSialorrheaRotarod Performance TestAxonsNoninvasive VentilationAmino Acid SubstitutionRibonuclease, PancreaticAxonal TransportNeuromuscular DiseasesCase-Control StudiesAnimals, Genetically ModifiedMuscle WeaknessMitochondriaAmino Acids, DiaminoCell DeathPeripherinsProtein FoldingScleroderma, SystemicPhenotypeElectromyographyLaughterMagnetic Resonance ImagingDementiaNeuromuscular JunctionNerve Tissue ProteinsNeurogliaCentral Nervous SystemParkinson DiseasePedigreeParalysisCommunication Aids for DisabledCopperMice, Inbred C57BLTracheostomyItalyGlial Fibrillary Acidic ProteinGliosisMuscle, SkeletalGlutamic AcidChromosomes, Human, Pair 9UbiquitinImmunohistochemistryAtrophyMotor CortexGenetic Predisposition to DiseasePyrazolonesRespiratory InsufficiencyMuscular Atrophy, SpinalOxidative StressNervous System DiseasesGlycineMultiple Sclerosis, Chronic ProgressiveCell SurvivalProteinsTime FactorsNeuroimagingMuscular Atrophy