Diseases
Susac SyndromeRetinal Artery OcclusionRetinal VasculitisSyndromeHearing Loss, SensorineuralBrain Diseases

Retinal and optic nerve head pathology in Susac's syndrome. (1/12)

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Severe retention hyperkeratosis occurring with Susac syndrome. (2/12)

A 50-year-old woman presented for asymptomatic yellow hyperkeratotic plaques limited to her face. The plaques reportedly arose over the six months prior to her clinic visit. She was healthy prior to the diagnosis of Susac syndrome (retinocochleocerebral vasculopathy) two years before. A punch biopsy was performed and revealed retention hyperkeratosis. Retention hyperkeratosis is a benign and commonly seen skin condition in primary care and dermatology. Retention hyperkeratosis occurs when there is abnormality of routine desquamation that can be associated with poor hygeine. It can be associated with acne or ichthyosis. Our case of retention hyperkeratosis is unique because of the profound presentation in a setting of an untreated psychiatric condition. Treatment consisted of daily topical exfoliative care. We also encouraged her family members to help her to seek medical attention for Susac syndrome.  (+info)

Letter: It is Dermatosis neglecta. (3/12)

The case presented in the article "Severe retention hyperkeratosis occurring with Susac syndrome" in October 2010 of DOJ (16:10) is very dramatic. Although it was implied in the article, the authors did not state that this is actually Dermatosis neglecta, the same entity reported by Poskitt et al 15 years ago. The description of the case in the article, histopathology, mechanism of pathogenesis, and treatment are consistent with Dermatosis neglecta, only with a different name.  (+info)

Temporal bone findings in a case of Susac's syndrome. (4/12)

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Recurrent bilateral branch retinal artery occlusion with hearing loss and encephalopathy: the first case report of Susac syndrome in Korea. (5/12)

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Susac syndrome: an organ-specific autoimmune endotheliopathy syndrome associated with anti-endothelial cell antibodies. (6/12)

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Patterns of retinal damage facilitate differential diagnosis between Susac syndrome and MS. (7/12)

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Susac's Syndrome: A Case Presentation and Radiological Approach to this Rare Autoimmune Endotheliopathy. (8/12)

Susac's syndrome is an uncommon neurologic disorder, consisting of the clinical triad of encephalopathy, branch retinal artery occlusions, and hearing loss. We report a case of a sudden vision and hearing impairment in a 35-year-old female patient. Magnetic resonance imaging of the brain revealed multiple lesions in the white matter and the corpus callosum, typical of Susac's syndrome.  (+info)