Hematopoietic stem cell transplantation practice variation among centers in the Eastern Mediterranean Region (EMRO): Eastern Mediterranean Bone Marrow Transplantation (EMBMT) group survey.
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Pulmonary venous atrial obstruction after the Senning procedure: relief by catheter balloon dilatation.
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Pulmonary venous atrial stenosis developed after a modified Senning procedure in an infant with transposition of the great arteries. The pulmonary venous atrium was surgically revised, but the obstruction recurred. The stenosis was then enlarged by percutaneous balloon catheter dilatation. There was an immediate haemodynamic and echocardiographic improvement. Clinical and echocardiographic improvement persisted nine months after dilatation. The procedure was complicated by staphylococcal endarteritis. (+info)
Balloon dilation of pulmonary venous pathway obstruction after Mustard repair for transposition of the great arteries.
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Percutaneous balloon dilation was attempted in three patients with mid baffle pulmonary venous pathway obstruction after the Mustard operation for transposition of the great arteries. The procedure was unsuccessful in a 3 year old boy. Evidence for relief of obstruction in the other two patients (7 and 14 years old, respectively) consisted of angiographic demonstration of improved caliber at the site of the pulmonary venous pathway narrowing, improvement in the Doppler spectral signal at this site from an "obstructed" to a "normal" pattern as well as symptomatic improvement. Balloon dilation was performed twice in one of these patients. The Doppler and symptomatic improvement were sustained in both patients at short-term follow-up (5 and 6 months, respectively). This technique may offer effective relief of pulmonary venous pathway obstruction in some patients with this complication of the Mustard operation. (+info)
Pulmonary veno-occlusive disease presenting with thrombosis of pulmonary arteries.
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Pulmonary veno-occlusive disease is a rare cause of pulmonary hypertension. An unusual case presenting with thrombosis of the right pulmonary artery and serological evidence of autoimmunity is reported. (+info)
Deringing procedure for congenital pulmonary vein stenosis.
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We operated on a 14-year-old boy who had an echocardiographic diagnosis of ventricular septal defect. At surgery we found, in addition, an anomalous and obstructive intraventricular muscle bundle. Detection of a continuous thrill over the right pulmonary veins, prior to cardiopulmonary bypass, led to exploration of the left atrium. The ostia of the right superior and inferior pulmonary veins were impeded by circumferential membranous rings of endocardium with central stenotic openings. Excision of these annular rings relieved the obstruction. The left lung was drained by a long intrapericardial common venous channel that entered the left atrium through a stenotic ostium; excision of an annular ridge of endocardium restored normal flow. The patient remains asymptomatic after 23 months. The case is reported for the new deringing technique and the rarity of successful correction of congenital pulmonary vein stenosis. (+info)
Transcatheter stent implantation for recurrent pulmonary venous pathway obstruction after the Mustard procedure.
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A 5 year old boy presented with obstruction of the pulmonary venous pathway four years after the Mustard procedure. A successful balloon dilatation of the pulmonary venous pathway was performed but the benefit was transient. Placement of a 10 mm balloon expandable intravascular stent across the recurrent stenosis resulted in complete relief of the obstruction with prompt resolution of the clinical signs. The delivery system was modified to facilitate stent delivery. (+info)
Pulmonary veno-occlusive disease: diagnosis during life in four patients.
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Pulmonary veno-occlusive disease is a rare form of primary pulmonary hypertension of unknown aetiology. Four cases were diagnosed in young patients. The diagnosis was suspected on the basis of clinical, radiological, echocardiographic, and catheter evidence and confirmed by taking a lung biopsy sample. In all patients the histology showed obstruction of the pulmonary veins by intimal fibrosis. The clinical course of all patients has been one of progressive deterioration. Although there is no specific treatment for this disease, to establish the diagnosis during life is of great importance in overall clinical management, including counselling the patient and family. (+info)