Wegener GranulomatosisLymphomatoid GranulomatosisAntibodies, Antineutrophil CytoplasmicMyeloblastinVasculitisMicroscopic PolyangiitisGranulomatosis, OrofacialChurg-Strauss SyndromePolyarteritis NodosaHistiocytosis, Langerhans-CellSarcoidosisGranulomaScleritisCryopyrin-Associated Periodic SyndromesNose Deformities, AcquiredImmunosuppressive AgentsAnti-Neutrophil Cytoplasmic Antibody-Associated VasculitisSerine EndopeptidasesBronchial DiseasesLaryngostenosisLung DiseasesSyndromeCyclophosphamidePrednisoloneBehcet SyndromePeroxidaseSarcoidosis, PulmonaryOrbital DiseasesArteritisEosinophilic GranulomaBiopsyNose DiseasesSkin DiseasesVasculitis, Leukocytoclastic, CutaneousGranuloma, Respiratory TractAutoantibodiesFatal OutcomeSystemic VasculitisPseudoxanthoma ElasticumLip DiseasesGlomerulonephritisTomography, X-Ray ComputedTreatment OutcomeAllostasisRecurrenceAutoantigensMyotonic DisordersEye DiseasesCranial Nerve DiseasesIleal DiseasesMyotonic DystrophySkin ManifestationsAlagille SyndromeMultiple TraumaPrednisoneGranuloma, Lethal MidlineFocal Dermal HypoplasiaAntibodies, Monoclonal, Murine-DerivedMethylprednisoloneHorner SyndromeRemission InductionGlycogen Storage Disease Type IIbNeutrophilsOtorhinolaryngologic DiseasesOphthalmoplegiaFacial ParalysisTalcHobbiesKidneys, ArtificialAdrenal Cortex HormonesLymphangioleiomyomatosisRetrospective StudiesCongenital Disorders of GlycosylationMouth DiseasesFluorescent Antibody Technique, IndirectDe Lange SyndromeAzathioprineTuberous SclerosisGlucocorticoidsParanasal SinusesAutoimmune DiseasesLeukocyte Elastase